Baruchel S, Rees J, Bernstein M L, Goodyer P
Division of Hematology, McGill University, Montreal, Quebec, Canada.
Am J Pediatr Hematol Oncol. 1993 Feb;15(1):115-6. doi: 10.1097/00043426-199302000-00017.
We report a 16-year-old Tanner IV male with homozygous hemoglobin S who presented with recurrent episodes of priapism unresponsive to standard therapy with hydration, analgesia, and exchange transfusion. He had a complete resolution of his symptoms with hydralazine therapy. We therefore suggest a trial of vasodilator therapy for recurrent sickle cell priapism before attempting surgical therapy.
