Kurzhals G, Maciejewski W, Agathos M, Meurer M, Mily H, Breit R
Dermatologische und Allergologische Abteilung, Städtisches Krankenhaus München-Schwabing, Ludwig-Maximilians Universität München.
Hautarzt. 1993 Feb;44(2):110-3.
Localized cicatricial pemphigoid of the Brunsting-Perry type is a very rare bullous condition, which has so far been reported in 51 cases. It is characterized by scarring blisters confined to the head, scalp and neck. Diagnosis can be difficult because of the discrete skin lesions, often repeatedly false-negative direct immunofluorescence, and the absence of circulating antibodies. We report on a 87-year-old male patient with the typical clinical feature of a cicatricial pemphigoid of the Brunsting-Perry type and give a review of the 51 cases published in the world literature.
布伦斯廷-佩里型局限性瘢痕性类天疱疮是一种非常罕见的大疱性疾病，迄今为止共报道了51例。其特征为瘢痕性水疱局限于头部、头皮和颈部。由于皮肤损害不连续、直接免疫荧光检查常呈反复假阴性以及缺乏循环抗体，诊断可能会很困难。我们报告了一名87岁男性患者，其具有布伦斯廷-佩里型瘢痕性类天疱疮的典型临床特征，并对世界文献中发表的51例病例进行了综述。
