Kumar A, Kruger L M
Shriners Hospital for Crippled Children, Springfield, Massachusetts 01104.
J Pediatr Orthop. 1993 Mar-Apr;13(2):203-9.
Longitudinal deficiency of the tibia associated with fibular dimelia is a very rare condition. We report our experience with six patients and outline management of this anomaly. Knee disarticulation is advised in cases with an associated normal femur, and femorofibular fusion is advised in cases of associated ipsilateral proximal focal femoral deficiency (PFFD) or congenital short femur. Fibulocalcaneal fusion and Boyd type amputation provide good end-bearing stumps.