Cohn D
Med J Aust. 1977 Jan 22;1(4):101-4. doi: 10.5694/j.1326-5377.1977.tb130534.x.
A case (including autopsy findings) is reported of multilobular biliary cirrhosis with a strictly nodular liver developing in a 20-year-old male with cystic fibrosis (mucoviscidosis). The pathogenesis of biliary cirrhosis in cystic fibrosis is briefly discussed.
报告了一例20岁男性囊性纤维化(黏液黏稠病)患者发生的多小叶性胆汁性肝硬化伴肝脏呈严格结节状的病例(包括尸检结果)。简要讨论了囊性纤维化中胆汁性肝硬化的发病机制。