Lüftner J, Scheibner K, Wöckel W
Zentralbl Allg Pathol. 1977;121(1-2):195-200.
In 25 cases of autoptically proven mucoviscidosis 3 cases were detected with hepatic infestation. In two cases there was a focal biliary fibrosis (one male baby of 3 months, one female baby of 8 months), the third case was a 7 1/2 years old boy with a multilobulary biliary cirrhosis. The morphologie picture of these lesions is described, and their frequency, etiology and pathogenesis are discussed. Secondary alterations of the liver are for more frequent in this disorder than real liver infestations of mucoviscidosis, possible implications of this fact are shortly mentioned, too.