Santacana E, Jiménez M, Vilanova F, Villar Landeira J M
Servicio de Anestesiología, Reanimación y Terapéutica del Dolor, Hospital de la Santa Creu i Sant Pau, Barcelona.
Rev Esp Anestesiol Reanim. 1993 Jan-Feb;40(1):26-8.
Periodic familial hyperpotassemic paralysis is a dominant autosomic disease of brief periods of acute flaccid paralysis with complete posterior recovery. During surgical-anesthesia a number of factors concur which may trigger a paralytic episode. To this effect anesthetic drugs such as barbiturates and muscle relaxants have been involved. The case of a 12 year old patient with familial hyperpotassemic paralysis who received general anesthesia with propofol and atracurium besylate for emergency appendectomy is presented. During surgery the plasma levels of potassium were monitored and prophylaxis of the factors which potentially trigger a paralytic picture was performed. Both, the perioperative and the postoperative period, were without complications.
周期性家族性高钾性麻痹是一种常染色体显性疾病，表现为短暂的急性弛缓性麻痹，随后完全恢复。在外科麻醉期间，多种因素共同作用可能引发麻痹发作。为此，巴比妥类药物和肌肉松弛剂等麻醉药物与之有关。本文介绍了一名12岁家族性高钾性麻痹患者的病例，该患者因急诊阑尾切除术接受了丙泊酚和阿曲库铵苯磺酸盐全身麻醉。手术期间监测了血钾水平，并对可能引发麻痹症状的因素进行了预防。围手术期和术后均无并发症。
