Koelfen W, Freund M, Rohr H, Schultze C, Holthausen H
Universitäts-Kinderklinik, Mannheim.
Monatsschr Kinderheilkd. 1993 Apr;141(4):300-2.
Hemimegalencephaly is associated with a poor clinical course characterized by intractable seizures and severe encephalopathy. We present a case report of a girl with hemimegalencephaly. At the age of 9 month hemispherectomy was undertaken to preserve function of the other hemisphere. MRI and histologic examinations showed characteristic dysplastic malformations. Follow-up and the complications are described.
半侧巨脑症与以难治性癫痫和严重脑病为特征的不良临床病程相关。我们报告一例半侧巨脑症女孩的病例。9个月大时进行了大脑半球切除术以保留另一侧半球的功能。MRI和组织学检查显示出特征性的发育异常畸形。描述了随访情况及并发症。
