[塞扎里综合征]

[Sézary syndrome].

作者信息

Chen C C, Wang W J, Hwang W L, Chou G

机构信息

Department of Dermatology, National Yang-Ming Medical College.

出版信息

Zhonghua Yi Xue Za Zhi (Taipei). 1993 Mar;51(3):244-8.

PMID:8490802

Abstract

Sézary syndrome is a form of leukemia-lymphoma characterized clinically by erythroderma, pruritus, adenopathy, and circulating atypical cells with cerebriform nuclei. Histologically, atypical lymphocytes in the dermis and Pautrier's microabscesses are often present in skin biopsy specimens. We herein report a typical case of Sézary syndrome showing T-suppressor-cell characteristics, and related literatures are reviewed.

摘要

覃样肉芽肿综合征是一种白血病性淋巴瘤，临床上以红皮病、瘙痒、淋巴结病以及循环出现的具有脑回状核的非典型细胞为特征。组织学上，皮肤活检标本中常可见真皮内的非典型淋巴细胞和波特里微脓肿。我们在此报告一例表现出T抑制细胞特征的覃样肉芽肿综合征典型病例，并对相关文献进行综述。