Beardshaw J A, Gibson D G, Pearson M C, Upton M T, Anderson R H
Br Heart J. 1977 Mar;39(3):266-75. doi: 10.1136/hrt.39.3.266.
Anatomical studies have shown that the pathognomonic feature of primitive ventricle is absence of that portion of the interventricular septum which interposes between the atrioventricular valves. The relation of this posterior septum to the atrioventricular valves is such that echocardiography should be a particularly suitable technique for showing its presence or absence. When a posterior septum is present, it is seen on an echocardiogram as a double echo between the two atrioventricular valves. It presence limits posterior movement of the septal cusp of the anterior atrioventricular valve. Absence of the posterior septum should, therefore, be seen echocardiographically as more than mere absence of the double septal echo. It should be possible to show unusual posterior excursion of the "septal" cusp of the anterior atrioventricular valve and apposition of the "septal" cusps of the atrioventricular valves during diastole. In most instances it should also be possible to demonstrate that the posterior great artery is in continuity with both atrioventricular valves. We have shown these echocardiographic features in 26 patients. The diagnosis of primitive ventricle has been confirmed at necropsy or at operation in 4 patients. In the other 22 patients in angiographic data are compatible with a diagnosis of primitive ventricle. Demonstration of these positive features at echocardiography is, therefore, of considerable value in the initial diagnosis of primitive ventricle and in particular its differentiation from other congenital malformations.
解剖学研究表明，原始心室的特征性表现是室间隔位于房室瓣之间的部分缺失。该后间隔与房室瓣的关系使得超声心动图应是显示其有无的特别合适的技术。当存在后间隔时，在超声心动图上可看到它表现为两个房室瓣之间的双重回声。它的存在限制了前房室瓣隔叶的向后运动。因此，超声心动图上后间隔的缺失不应仅仅表现为间隔双重回声的缺失。应该能够显示前房室瓣“隔叶”的异常向后移动以及舒张期房室瓣“隔叶”的贴合。在大多数情况下，还应该能够证明后大动脉与两个房室瓣相连续。我们在26例患者中显示了这些超声心动图特征。4例患者在尸检或手术时确诊为原始心室。在其他22例患者中，血管造影数据与原始心室的诊断相符。因此，超声心动图上这些阳性特征的显示在原始心室的初步诊断中，特别是在其与其他先天性畸形的鉴别中具有相当大的价值。
