Shoumaker R D, Ajax E T, Schenkenberg T
Dis Nerv Syst. 1977 Apr;38(4):293-9.
The selective inability to comprehend the spoken word, in the absence of aphasia or defective or defective hearing, is defined as pure word deafness (auditory verbal agnosia). Reported cases of this rare disorder have suggested the site of involvement to be strategically placed, interrupting fibers from left and right primary auditory receptive areas which project to Wernicke's are in the dominant hemisphere. Our patient is a 44-year-old male who suffered from an uncertain illness complicated by fever, jaundice and generalized seizures seven years previously. Following an apparent convulsion, the patient was noted to be unable to understand spoken language without loss of ability to recognize and respond to sounds or marked impairment of speech or reading. The evidence suggested bilateral cerebral hemisphere disease more marked on the right. The abrupt onset without progression is consistent with a vascular or ischemic etiology. Conclusions about the nature of the lesion and areas involved must await further studies and ultimately tissue examination.
在没有失语症或听力缺陷的情况下，选择性地无法理解口语，被定义为纯词聋（听觉性言语失认症）。关于这种罕见病症的报道病例表明，受累部位处于关键位置，中断了从左右初级听觉感受区投射到优势半球韦尼克区的纤维。我们的患者是一名44岁男性，7年前患有一种病因不明的疾病，伴有发热、黄疸和全身性癫痫发作。在一次明显的抽搐发作后，发现患者无法理解口语，但仍保留识别和对声音做出反应的能力，且言语或阅读无明显受损。证据表明双侧大脑半球疾病，右侧更为明显。起病突然且无进展符合血管性或缺血性病因。关于病变性质和受累区域的结论必须等待进一步研究，最终有待组织检查。
