Marhuenda C, Mir I, Perez A, Yeste D, Carreño J C, Gil-Vernet J M, Boix-Ochoa J
Departamento de Cirurgía Pediátrica, Hospital Infantil Vall d'Hebrón, Barcelona.
Cir Pediatr. 1993 Jan;6(1):44-5.
A 18 month-old boy with asplenic syndrome was admitted to our hospital with a twelve hours history of mucous vomiting, abdominal pain and a round epigastric mass. It was diagnosed as having a gastric volvulus and an emergency laparotomy was performed. The stomach was situated at the right side and a mesenterioaxial volvulus was found, with cyanosis of the antrum. The gastrophrenic and gastrosplenic ligaments were absent. The clinical and radiological characteristics of asplenic syndrome are reviewed. The pediatric surgeons must be aware of the digestive malformations of the asplenic syndrome, because some of that like malfixation of the stomach could be the cause of an acute abdomen.
一名18个月大的无脾综合征男孩因黏液性呕吐、腹痛及上腹部圆形肿块12小时的病史入院。诊断为胃扭转，遂行急诊剖腹手术。胃位于右侧，发现为系膜轴性扭转，胃窦部发绀。胃膈韧带和胃脾韧带缺如。本文回顾了无脾综合征的临床和放射学特征。小儿外科医生必须了解无脾综合征的消化畸形，因为其中一些如胃固定异常可能是急腹症的病因。
