大疱性表皮松解症的食管受累情况。

Oesophageal involvement in epidermolysis bullosa.

作者信息

Gnanapragasam A

出版信息

J Laryngol Otol. 1977 Mar;91(3):271-4. doi: 10.1017/s0022215100083663.

Abstract

Epidermolysis bullosa dystrophica causing oesophageal stricture in two males of a family of 4 siblings--2 females and 2 males, and whose parents are not related, is reported. The stricture was treated with repeated dilatations and oral prednisolone on and off with complete success. A brief comment is also made with regards to the pathology and management of this condition.

摘要

据报道，在一个有4个兄弟姐妹（2名女性和2名男性）的家庭中，两名男性患有营养不良性大疱性表皮松解症并导致食管狭窄，其父母无血缘关系。通过反复扩张和间断口服泼尼松龙对狭窄进行治疗，取得了完全成功。文中还对该病的病理和治疗进行了简要评论。