Nelson L H, Dewan D M, Mandell G L
Department of Obstetrics and Gynecology, Bowman Gray School of Medicine, Wake Forest University, Winston-Salem, North Carolina 27157.
J Reprod Med. 1993 Apr;38(4):311-3.
The obstetric and anesthetic considerations in the management of a patient with the May-Hegglin anomaly, an autosomal dominant platelet deficiency, are discussed. A review of the medical literature notes three previous case reports of May-Hegglin anomaly in pregnancy. In addition to the two successful pregnancies reported in this paper, there are four infant survivors among the five reported pregnancies. Anesthetic managements included general and spinal anesthesia: the latter employed following platelet transfusion. A successful pregnancy should be anticipated when management includes a well-informed patient and coordinated obstetric and anesthetic care.
本文讨论了患有常染色体显性血小板缺乏症——May-Hegglin异常患者的产科和麻醉相关注意事项。医学文献回顾指出，此前有三篇关于May-Hegglin异常妊娠的病例报告。除本文报告的两例成功妊娠外，在报告的五例妊娠中有四名婴儿存活。麻醉管理包括全身麻醉和脊髓麻醉：后者在输注血小板后采用。当管理措施包括患者充分知情以及产科和麻醉护理协调配合时，有望实现成功妊娠。
