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[孤立性左位心合并左房异构、多脾畸形及法洛四联症的成功手术]

[A successful operation of isolated levocardia with left atrial isomerism, polysplenia and tetralogy of Fallot].

作者信息

Gojo S, Kawachi K, Fukutomi M, Kobayashi S, Hamada Y, Kitamura S

机构信息

Department of Surgery III, Nara Medical College, Japan.

出版信息

Nihon Kyobu Geka Gakkai Zasshi. 1993 Apr;41(4):655-9.

PMID:8515166
Abstract

A four-year-old boy who had isolated levocardia associated with left atrial isomerism, polysplenia and tetralogy of Fallot underwent successful corrective surgery. In addition, these anomalies were complicated by interrupted inferior vena cava, azygos continuation, and total anomalous hepatic venous connection. Because of these systemic venous anomalies, cardiopulmonary bypass presented us some problems of venous cannulations. We used 4 direct venous cannulations; i.e., superior vena cava, persistent left superior vena cava through coronary sinus, azygos vein and hepatic vein. Reports of total correction in patients with isolated levocardia associated with tetralogy of Fallot are rare, and we report the case with some reviews of the related literature.

摘要

一名患有孤立性左位心并伴有左心房异构、多脾和法洛四联症的4岁男孩接受了成功的矫正手术。此外,这些异常还合并有下腔静脉中断、奇静脉延续和完全性肝静脉异常连接。由于这些体静脉异常,体外循环给我们带来了一些静脉插管问题。我们采用了4根直接静脉插管,即上腔静脉、经冠状窦的永存左上腔静脉、奇静脉和肝静脉。关于孤立性左位心合并法洛四联症患者进行完全矫正的报道很少,我们报告了该病例并对相关文献进行了一些综述。

相似文献

1
[A successful operation of isolated levocardia with left atrial isomerism, polysplenia and tetralogy of Fallot].[孤立性左位心合并左房异构、多脾畸形及法洛四联症的成功手术]
Nihon Kyobu Geka Gakkai Zasshi. 1993 Apr;41(4):655-9.
2
[A case of successful surgery for tetralogy of Fallot with single atrium, azygous connection and partial anomalous pulmonary venous drainage in atrio-visceral heterotaxic syndrome].[一例心房内脏异位综合征合并法洛四联症、单心房、奇静脉连接及部分肺静脉异位引流的成功手术病例]
Kyobu Geka. 1992 Nov;45(12):1103-5.
3
[A successful correction of common atrium with left atrial isomerism].[成功矫正左心房异构型共同心房]
Kyobu Geka. 1991 Nov;44(12):1052-5.
4
[Tetralogy of Fallot associated with left atrial isomerism].法洛四联症合并左心房异构
Arq Bras Cardiol. 1996 Oct;67(4):249-53.
5
[Successful repair of total anomalous pulmonary venous connection and incomplete endocardial cushion defect associated with left isomerism].[成功修复与左心异构相关的完全性肺静脉异位连接及不完全性心内膜垫缺损]
Kyobu Geka. 1993 May;46(5):442-4.
6
[A surgical case report--rare association of tetralogy of Fallot with cor triatriatum, unroofed coronary sinus and persistent left superior vena cava].[一例手术病例报告——法洛四联症合并三房心、冠状静脉窦未闭及永存左上腔静脉的罕见关联]
Nihon Kyobu Geka Gakkai Zasshi. 1997 Jan;45(1):92-5.
7
[Successful repair of isolated levocardia associated with ventricular septal defect, interrupted inferior vena cava and azygos continuation].[成功修复与室间隔缺损、下腔静脉中断和奇静脉延续相关的孤立性左旋心]
Kyobu Geka. 1988 Feb;41(2):158-61.
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Radionuclide angiography of azygos continuation of inferior vena cava in left atrial isomerism (polysplenia syndrome).左心房异构(多脾综合征)下腔静脉奇静脉延续的放射性核素血管造影。
Clin Nucl Med. 1987 Sep;12(9):708-10. doi: 10.1097/00003072-198709000-00006.
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Intraatrial baffle repair of isolated ventricular inversion with left atrial isomerism.采用左心房异构的孤立性心室反位的心房内挡板修复术。
Ann Thorac Surg. 1996 Nov;62(5):1529-32. doi: 10.1016/0003-4975(96)00546-2.
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Double-outlet right atrium associated with tetralogy of Fallot and common atrioventricular valve.右心房双出口合并法洛四联症及共同房室瓣。
J Thorac Cardiovasc Surg. 1986 Feb;91(2):205-7.

引用本文的文献

1
Left isomerism with bilateral superior vena cava, interrupted inferior vena cava and tetralogy of Fallot.左位异构合并双侧上腔静脉、下腔静脉中断及法洛四联症。
Ann Pediatr Cardiol. 2020 Oct-Dec;13(4):364-367. doi: 10.4103/apc.APC_117_20. Epub 2020 Sep 17.
2
Tetralogy of Fallot with isolated levocardia in a young female.一名年轻女性患法洛四联症伴孤立性左位心。
J Community Hosp Intern Med Perspect. 2019 Jun 19;9(3):275-278. doi: 10.1080/20009666.2019.1601980. eCollection 2019.