Barranco Simó M J, Ciscar Vilanova M A, Ibor Otamendi J L, Ferrando Marco J, Juan Samper G
Servicio de Neumología, Hospital General, Valencia.
An Med Interna. 1993 May;10(5):240-2.
Pulmonary lymphangioleiomyomatosis (PLLM) is characterized by a benign proliferation of the smooth muscle around lymphatics, venulas and bronchiolus. It is usually fatal within 1 to 9 years. We present a case which remained with scarce symptoms despite receiving no treatment after at least 9 years of evolution of the disease. We highlight the clinical manifestations of the disease and the relevance of pulmonary biopsia with thoracotomy in order to establish the diagnosis.
肺淋巴管平滑肌瘤病（PLLM）的特征是淋巴管、小静脉和细支气管周围的平滑肌良性增生。该病通常在1至9年内致死。我们报告一例病例，该患者在疾病进展至少9年后未接受治疗，但症状轻微。我们强调了该疾病的临床表现以及开胸肺活检对确诊的重要性。
