A fatal case of portal hypertension complicating systemic mastocytosis in an adolescent.
作者信息
Fonga-Djimi H S, Gottrand F, Bonnevalle M, Farriaux J P
机构信息
Service de Pédiatrie, Hôpital Huriez, Lille, France.
出版信息
Eur J Pediatr. 1995 Oct;154(10):819-21. doi: 10.1007/BF01959789.
PMID:8529680
Abstract
Portal hypertension was observed in a 17-year-old girl with urticaria pigmentosa since 2 months of age. Liver biopsies showed portal and sinusoidal infiltration with mast cells although spleen biopsies showed only fibrosis. CONCLUSION. Portal hypertension is a complication of systemic mastocytosis that can lead to death. Treatment with interferon alpha might be effective.
摘要
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