Pascual-Castroviejo I, Pascual-Pascual S I, Viaño J, Martinez V, Coya J
Service of Pediatric Neurology, Hospital Infantil La Paz, Madrid, Spain.
Neuropediatrics. 1995 Aug;26(4):220-2. doi: 10.1055/s-2007-979759.
A patient with Sturge-Weber syndrome without the characteristic facial nevus presented with focal seizures which were difficult to control and borderline mental level. CT disclosed calcification in the right occipital zone. A marked decrease of the regional cerebral blood flow that extended beyond the abnormalities depicted on CT was seen by SPECT. Venous magnetic resonance (MR) angiography revealed reduction of the superficial cortical veins and prominent deep collateral venous system in the same side of the cerebral lesion. Cranial MR imaging with Gd-DTPA demonstrated the pial angioma.
一名患有斯特奇-韦伯综合征但无典型面部痣的患者出现局灶性癫痫发作，难以控制，且智力水平处于临界状态。CT显示右侧枕叶区域有钙化。SPECT显示局部脑血流量显著减少，范围超出CT所示异常区域。静脉磁共振血管造影显示脑病变同侧的浅表皮质静脉减少，深部侧支静脉系统明显。使用钆喷酸葡胺进行的头颅磁共振成像显示了软脑膜血管瘤。
