Chang R Y, Tsai C H, Chou Y S, Wu T C
Department of Internal Medicine, Mackay Memorial Hospital, Taipei, Taiwan, R.O.C.
Angiology. 1996 Jan;47(1):87-92. doi: 10.1177/000331979604700114.
Idiopathic dilatation of the pulmonary artery is an uncommon, but not rare, congenital anomaly that is diagnosed by exclusion and generally has a benign clinical course. A left hilar mass on the chest x-ray film is the major presentation. The authors present a case of idiopathic dilatation of the pulmonary artery with posttraumatic chest pain clinically. After serial examinations, idiopathic dilatation of the pulmonary artery was diagnosed. They discuss the phenomenon of transpulmonary valvular pressure gradient and noninvasive tools for long-term follow-up, including transesophageal echocardiography and magnetic resonance imaging.
特发性肺动脉扩张是一种不常见但也不罕见的先天性异常，通过排除法诊断，通常具有良性临床病程。胸部X线片上的左肺门肿块是主要表现。作者报告了一例临床上伴有创伤后胸痛的特发性肺动脉扩张病例。经过一系列检查，诊断为特发性肺动脉扩张。他们讨论了跨肺动脉瓣压力阶差现象以及用于长期随访的非侵入性工具，包括经食管超声心动图和磁共振成像。
