da Silveira W L, Ostoa D E, Jatene M B, Barbero-Marcial M, Oliveira S A, Jatene A D
Instituto do Coração do Hospital das Clínicas, FMUSP.
Arq Bras Cardiol. 1995 Jul;65(1):31-5.
To evaluate the surgical result of the cases of congenital fistulae of the coronary artery.
Seven patients were surgically treated since January 80 until February 94. The ages ranged from 3 days to 52 years old. The diagnosis was suspected by echocardiogram and established by cardiac catheterization.
Regarding the clinical status, 3 (42.85%) patients were asymptomatic, 3 (42.85%) presented congestive heart failure and 1 (14.28%) precordial pain and palpitation. The fistulae, located in inferior wall of the right ventricle in 1 (14.28%) patient, apex of the right ventricle in 1 (14.28%), right atrium in 3 (42.85%), and coronary sinus in 1 (14.28%), were isolated in 4 (57.17%), 1 (14.28%) also had fixed subaortic stenosis, 1 (14.28%) had previously undergone the ligate of the ductus arteriosus and 1 (14.28%) also had aortic coarctation and ductus arteriosus. After surgical treatment, 5 (85.72%) had follow up abnormalities, showing good clinical outcome; 1 (14.28%), that also had aortic and subaortic stenosis, followed with minimal aortic regurgitation and poor left ventricular performance; 1 (14.28%), that had aortic coarctation and ductus arteriosus, who had been operated on in unfavourable hemodynamic conditions, died 5 days after surgery.
Surgical correction should be proposed as a treatment of the congenital fistulae of the coronary artery, since it is technically feasible, and has low in-hospital mortality and morbidity.
评估先天性冠状动脉瘘病例的手术结果。
自1980年1月至1994年2月,对7例患者进行了手术治疗。年龄范围为3天至52岁。通过超声心动图怀疑诊断,并通过心导管检查确诊。
就临床状况而言,3例(42.85%)患者无症状,3例(42.85%)出现充血性心力衰竭,1例(14.28%)有心前区疼痛和心悸。瘘管位于右心室下壁1例(14.28%),右心室尖1例(14.28%),右心房3例(42.85%),冠状窦1例(14.28%)。4例(57.17%)瘘管被隔离,1例(14.28%)同时合并固定性主动脉瓣下狭窄,1例(14.28%)既往曾行动脉导管结扎术,1例(14.28%)同时合并主动脉缩窄和动脉导管未闭。手术治疗后,5例(85.72%)随访无异常,临床结果良好;1例(14.28%)同时合并主动脉瓣和主动脉瓣下狭窄,随访有轻度主动脉瓣反流,左心室功能较差;1例(14.28%)合并主动脉缩窄和动脉导管未闭,在不利的血流动力学条件下接受手术,术后5天死亡。
由于先天性冠状动脉瘘手术技术可行,住院死亡率和发病率低,应建议手术矫正作为其治疗方法。