Serratrice G, Pouget J, Pellissier J F
Cliniques des Maladies du Système Nerveux et de l'Appareil Locomoteur, Marseille, France.
J Neurol Neurosurg Psychiatry. 1996 Jan;60(1):51-4. doi: 10.1136/jnnp.60.1.51.
Eight elderly patients developed progressive paravertebral muscle weakness with bent spine on standing but normal supine posture. Computed tomography showed pronounced hypodensity of the paraspinal muscles. Serum creatine kinase was moderately increased, paraspinal EMG non-specific, and biopsy myopathic. The syndrome was familial in two patients and may be caused by a late onset paraspinal muscle dystrophy. In the absence of specific pathological changes, such cases could be classified as having "bent spine syndrome".
8例老年患者出现渐进性椎旁肌无力，站立时脊柱弯曲，但仰卧姿势正常。计算机断层扫描显示椎旁肌肉明显低密度。血清肌酸激酶中度升高，椎旁肌电图无特异性，活检显示为肌病。该综合征在2例患者中具有家族性，可能由迟发性椎旁肌营养不良引起。在缺乏特异性病理改变的情况下，此类病例可归类为“脊柱弯曲综合征”。
