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[一名17岁男孩的罗萨伊-多夫曼综合征作为淋巴结病的诊断问题]

[Rosai-Dorfman syndrome in a 17 year old boy as a diagnostic problem of lymphadenopathy].

作者信息

Hicke A, Wieczorek M, Olejnik I

机构信息

Oddziału Hematologii Kliniki Pediatrii i Hematologii w Zabrzu.

出版信息

Acta Haematol Pol. 1995;26(4):425-8.

PMID:8571745
Abstract

Rosai-Dorfman syndrome of Sinus Histiocytosis with Massive Lymphadenopathy is a benign disorder of unknown etiology which is characterized by proliferation of phagocytic-like cells that infiltrate tissues. We present here a case of a 17 years old boy with the enlargement of the cervical lymph nodes who developed this disease. The diagnosis was established by the histopathological examination. There was no evidence of recurrence during the 18 months of follow up.

摘要

伴有巨大淋巴结病的窦性组织细胞增多症的罗萨伊-多尔夫曼综合征是一种病因不明的良性疾病,其特征是浸润组织的吞噬样细胞增殖。我们在此报告一例17岁患有颈部淋巴结肿大并罹患此病的男孩。诊断通过组织病理学检查确立。在18个月的随访期间没有复发迹象。

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