Megerian C A, Sofferman R A, McKenna M J, Eavey R D, Nadol J B
Department of Otolaryngology, Massachusetts Eye and Ear Infirmary, Boston 02114, USA.
Am J Otol. 1995 Jul;16(4):408-19.
monostotic. Although most patients had a conductive hearing loss, 17% of patients demonstrated profound sensorineural hearing loss ascribable to the lesion, and facial nerve sequelae were noted in nearly 10% of cases. Cholesteatoma complicated almost 40% of cases, usually in the form of a canal cholesteatoma. Ten new cases of temporal bone fibrous dysplasia are described not only to further clarify the spectrum of otologic sequelae but also to help illustrate available treatment options. In addition, this report documents, in three new cases, the previously undescribed progression of conductive hearing loss to profound sensorineural deafness secondary to fibrous dysplasia.
单骨型。尽管大多数患者有传导性听力损失，但17%的患者出现了因病变导致的重度感音神经性听力损失，近10%的病例出现了面神经后遗症。胆脂瘤在近40%的病例中并发，通常表现为外耳道胆脂瘤。本文描述了10例颞骨纤维发育不良的新病例，不仅是为了进一步明确耳科后遗症的范围，也是为了说明可用的治疗选择。此外，本报告记录了3例新病例中，以前未描述过的因纤维发育不良导致的传导性听力损失进展为重度感音神经性耳聋的情况。
