Moreau S, Bourdon N, Goullet de Rugy M, Bequignon A, Babin E, Valdazo A
Service ORL, CHU, Caen.
Ann Otolaryngol Chir Cervicofac. 1997;114(4):140-3.
Craniofacial fibrous dysplasia manifests clinically with dysmorphic syndrome, ophtalmologic or otologic signs. We report a case of temporal polyostotic fibrous dysplasia with vertigo and sensorineural hearing loss. Sensorineural hearing loss, with no cholesteatoma associated, as described in our case is rarely described. We review the literature concerning main clinical, diagnostic and therapeutic aspects of this disease.
颅面骨纤维发育不良在临床上表现为畸形综合征、眼科或耳科症状。我们报告一例伴有眩晕和感音神经性听力损失的颞骨多骨型纤维发育不良病例。如我们病例中所描述的，伴有感音神经性听力损失且无胆脂瘤相关情况很少被描述。我们回顾了关于该疾病主要临床、诊断和治疗方面的文献。
