Tape M W, Tye E
University of Texas, Houston, USA.
Compend Contin Educ Dent. 1995 May;16(5):524-8.
Ectodermal dysplasia is a group of rare inherited disorders that affect various tissues of ectodermal origin. The mode of inheritance varies among the different disorders. The most common form of ectodermal dysplasia is hypohidrotic ectodermal dysplasia (HED), which most severely affects the hair, nails, teeth, and skin. Men are more often and more severely affected than women. However, transmission is from the female carrier, who usually appears normal and unaffected. Dental treatment for these patients varies on an individual basis. This article illustrates a case of overdentures in a 7-year-old boy with HED.
外胚层发育不全是一组罕见的遗传性疾病,会影响外胚层起源的各种组织。不同疾病的遗传方式各不相同。外胚层发育不全最常见的形式是少汗型外胚层发育不全(HED),它对头发、指甲、牙齿和皮肤的影响最为严重。男性比女性更常受到影响且症状更严重。然而,该病是由女性携带者传播的,她们通常看起来正常且未受影响。这些患者的牙科治疗因个体而异。本文阐述了一名患有HED的7岁男孩佩戴覆盖义齿的病例。