Lhermitte-Duclos病的术前磁共振成像诊断：伴有血管扩张和空洞形成的病例报告
Preoperative MRI diagnosis of Lhermitte-Duclos disease: case report with associated enlarged vessel and syrinx.
作者信息
Wolansky L J, Malantic G P, Heary R, Maniker A H, Lee H J, Sharer L R, Patel U J
机构信息
Department of Radiology, UMDNJ-New Jersey Medical School, Newark 070103, USA.
出版信息
Surg Neurol. 1996 May;45(5):470-5; discussion 475-6. doi: 10.1016/0090-3019(95)00244-8.
BACKGROUND
The most common primary cerebellar tumor is hemangioblastoma, a lesion which is associated with magnetic resonance imaging (MR)-detectable vascularity in over 60%. Lhermitte-Duclos disease is an uncommon cause of a cerebellar mass that is not typically vascular.
METHODS
Computed tomography (CT), MRI with and without contrast, and magnetic resonance venography was performed in a patient with a cerebellar mass.
RESULTS
The cerebellar mass was noted to have a prominent vessel, as well as an associated syrinx. In spite of MRI-detectable vascularity, the striped appearance of the lesion was felt to be typical of Lhermitte-Duclos disease. At surgery, the mass was resected and the diagnosis of Lhermitte-Duclos disease was confirmed.
CONCLUSIONS
The diagnosis of Lhermitte-Duclos disease should be made when MRI shows a parallel linear "tiger-striped" lesion of the cerebellum. The presence of an enlarged vessel and/or syrinx should not deter one from making the preoperative diagnosis.
背景
最常见的原发性小脑肿瘤是血管母细胞瘤，超过60%的该病变与磁共振成像（MR）可检测到的血管有关。Lhermitte-Duclos病是小脑肿块的一种罕见病因，通常无血管表现。
方法
对一名患有小脑肿块的患者进行了计算机断层扫描（CT）、有无对比剂的MRI以及磁共振静脉造影。
结果
发现小脑肿块有一条明显的血管以及一个相关的空洞。尽管MRI可检测到血管，但该病变的条纹状外观被认为是Lhermitte-Duclos病的典型表现。手术中，切除了肿块，确诊为Lhermitte-Duclos病。
结论
当MRI显示小脑有平行线性“虎条纹”病变时，应诊断为Lhermitte-Duclos病。血管增粗和/或空洞的存在不应妨碍术前诊断。
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