Tost F, Weidlich R, Tost M
Klinik und Poliklinik, Augenkrankheiten der Martin-Luther-Universität Halle-Wittenberg.
Klin Monbl Augenheilkd. 1996 Feb;208(2):117-9. doi: 10.1055/s-2008-1035181.
There are various malformations of retinal vessels. Some of them are associated with cerebral vascular anomalies.
This report is given on a girl 6 years of age with a retinal racemose angioma.
The clinical examination showed a unilateral racemose angioma combined with retinachorioidal anastomosis and a hemifacial vascular malformation. We found teleangiectasia in this area. The ophthalmoscopy demonstrated a blurred border of optic disc on the right eye with forward protrusion of the disc about + 2.0 dioptres. Large racemose lesions may be localized to the optic nerve and may involve segmental areas of the macula. The ultrasound showed a papillary stasis with highly reflective structures. The ultrasonic patterns are interpreted as a cholesterosis or fibrovascular tissue. This findings may belong to the rare Wyburn-Mason syndrome. Acute neurological symptoms by similar lesions the midbrain and hemorrhages during extraction of teeth are reported in literature.
视网膜血管存在多种畸形。其中一些与脑血管异常相关。
本文报告一名6岁女孩患有视网膜蔓状血管瘤。
临床检查显示单侧蔓状血管瘤合并视网膜脉络膜吻合以及半侧面部血管畸形。我们在该区域发现了毛细血管扩张。检眼镜检查显示右眼视盘边界模糊，视盘向前突出约+2.0屈光度。大的蔓状病变可能局限于视神经，也可能累及黄斑的节段区域。超声显示乳头淤滞伴高反射结构。超声图像被解释为胆固醇沉着症或纤维血管组织。这些发现可能属于罕见的怀伯恩 - 梅森综合征。文献报道了由中脑类似病变引起的急性神经症状以及拔牙时的出血情况。
