薄层计算机断层扫描可在被认为患有青少年肾单位肾痨的患者中检测到髓质囊肿。

Thin-section computed tomography scans detect medullary cysts in patients believed to have juvenile nephronophthisis.

作者信息

Elzouki A Y, al-Suhaibani H, Mirza K, al-Sowailem A M

机构信息

Department of Pediatrics, King Fahad National Guard Hospital, Riyadh, Saudi Arabia.

出版信息

Am J Kidney Dis. 1996 Feb;27(2):216-9. doi: 10.1016/s0272-6386(96)90543-0.

DOI:10.1016/s0272-6386(96)90543-0

PMID:8659496

Abstract

Juvenile nephronophthisis (NPH) and medullary cystic kidney disease are an important cause of chronic renal failure in children and young adults. Medullary cysts are regarded as the hallmark of this condition. The diagnostic techniques that were used previously were not conclusive in most cases to demonstrate medullary cysts. We studied the role of thin-section (1.5-mm) computed tomography (CT) scan as an optimal imaging diagnostic technique. Three children who were admitted to our hospital consecutive with a clinical diagnosis of NPH were included. We found that the thin-section CT scan demonstrates the medullary cysts in all patients. We recommend CT scan as the investigation of choice in patients with clinical features suggestive of nephronophthisis-cystic renal medulla complex.

摘要

青少年肾单位肾痨（NPH）和髓质囊性病是儿童和年轻成人慢性肾衰竭的重要病因。髓质囊肿被视为这种疾病的标志。以前使用的诊断技术在大多数情况下无法确凿地显示髓质囊肿。我们研究了薄层（1.5毫米）计算机断层扫描（CT）作为一种最佳成像诊断技术的作用。纳入了连续3名因临床诊断为NPH而入住我院的儿童。我们发现薄层CT扫描能显示所有患者的髓质囊肿。我们建议，对于具有提示肾单位肾痨-囊性肾髓质综合征临床特征的患者，CT扫描是首选的检查方法。