Henderson M A
Department of Anaesthesia, Nambour General Hospital, Australia.
Eur J Anaesthesiol. 1995 Nov;12(6):613-6.
The mucopolysaccharidoses are a rare group of diseases. The Hunter Syndrome (mucopolysaccharidosis II) has been classified into severe and mild forms with presentation between the years 2 and 4. Enzyme assays provide the definitive diagnosis. An outstanding concern for the anaesthetist is airway management. The management of a patient with this condition is illustrated with a case report.
黏多糖贮积症是一类罕见的疾病。亨特综合征(黏多糖贮积症II型)已被分为重型和轻型,发病年龄在2至4岁之间。酶测定可提供明确诊断。麻醉医生特别关注的是气道管理。本文通过一则病例报告阐述了对此类患者的管理。