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脊髓性肌萎缩症患儿的心电图表现

Electrocardiographic findings in children with spinal muscular atrophy.

作者信息

Huang J J, Jong Y J, Huang M Y, Chiang C H, Huang T Y

机构信息

Department of Family Medicine, Kaohsiung Medical College, Taiwan.

出版信息

Jpn Heart J. 1996 Mar;37(2):239-42. doi: 10.1536/ihj.37.239.

DOI:10.1536/ihj.37.239
PMID:8676550
Abstract

Most of the patients in this study with spinal muscular atrophy were found to have tremors of the isoelectric line in the electrocardiogram (ECG) tracings. There were a total of 47 cases of SMA (mean age 40.8 months). All three types of SMA had a similar incidence (about 80%) of tremors in the tracings (p = 0.885). In 7 cases the ECG tremors had an intermittent pattern. ECG tremors were commonly found in the majority of SMA patients and this finding, though non-specific, may suggest a possible SMA diagnosis.

摘要

本研究中大多数脊髓性肌萎缩症患者在心电图(ECG)描记图中被发现等电位线有震颤。共有47例脊髓性肌萎缩症患者(平均年龄40.8个月)。所有三种类型的脊髓性肌萎缩症在描记图中震颤的发生率相似(约80%)(p = 0.885)。7例患者的心电图震颤呈间歇性模式。心电图震颤在大多数脊髓性肌萎缩症患者中普遍存在,这一发现虽然不具有特异性,但可能提示脊髓性肌萎缩症的诊断。

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