Diaz-Lobato S, Dorgham A, Garcia-Tejero M T, Redondo M A, Echevarri C, Martínez J, Corral J, Vázquez C
Servicio de Neumología, Hospital La Paz, Madrid.
Rev Neurol. 1996 May;24(129):562-3.
The clinical course of Duchenne's dystrophy is characterized by respiratory insufficiency secondary to failure of the breathing pump. Up to ten years ago, this respiratory insufficiency was corrected by mechanical ventilation via a tracheostomy. In recent years, nasal mechanical ventilation has been a considerable advance in the treatment of these patients' respiratory problems. We describe a patient with Duchenne's dystrophy who was satisfactorily treated by non-invasive mechanical ventilation.
杜兴氏肌营养不良症的临床病程以呼吸泵功能衰竭继发的呼吸功能不全为特征。直到十年前，这种呼吸功能不全是通过气管切开术进行机械通气来纠正的。近年来，鼻罩机械通气在治疗这些患者的呼吸问题方面取得了显著进展。我们描述了一名通过无创机械通气得到满意治疗的杜兴氏肌营养不良症患者。
