Rupprecht E, Wunderlich P, Dietzsch H J, Hennig K, Platzbecker H, Berger G, Leupold W, Wünsche W
Z Erkr Atmungsorgane. 1977;147(1):57-72.
In the light of 8 observations, made by the authors, vasoanomalies underlying the syndrome of the unilateral hyperlucent lung are discussed in their correlation to homolateral bronchial lesions. There were 3 cases with unilateral aplasia of the pulmonary artery in which the unilateral hyperlucency was found always on the healthy side. In these cases there was a normal bronchogram on both sides. The vascularization by the bronchial arteries causes characteristic changes both in the X-ray-picture and endoscopy. Hypoplasia of the pulmonary artery occurring simultaneously with hyperlucency of the affected side of the lung was found in five cases, 4 times in connection with homolateral, severe, diffuse deforming bronchitis and bronchiectases and 1 case with congenital bronchus stenosis. There is the opinion that besides a congenital form of the hypoplasia of the pulmonary artery a (virus?) --pneumonia, acquired in early childhood, can lead to a pulmonary hypoplasia and a bronchopulmonary dysplasia. The diagnosis can be made only after several special examinations performed in a multi-step system. The significance of the lung scintigraphy within the scope of this complex diagnostics is especially emphasized. Indication for surgery should be made very cautiously. Antibiotic long-term therapy and dsipensary care are considered to be essential.
根据作者所做的8项观察，探讨了单侧肺透亮度增高综合征潜在的血管异常与同侧支气管病变的相关性。有3例肺动脉单侧发育不全，单侧肺透亮度增高总是出现在健康侧。在这些病例中，双侧支气管造影均正常。支气管动脉供血在X线片和内镜检查中均引起特征性改变。5例发现肺动脉发育不全同时伴有患侧肺透亮度增高，其中4例伴有同侧严重弥漫性变形支气管炎和支气管扩张，1例伴有先天性支气管狭窄。有一种观点认为，除了先天性肺动脉发育不全形式外，儿童早期获得性（病毒？）肺炎可导致肺发育不全和支气管肺发育不良。只有在多步骤系统中进行多项特殊检查后才能做出诊断。特别强调了肺闪烁扫描在这一综合诊断中的意义。手术指征应非常谨慎地确定。长期抗生素治疗和门诊护理被认为是必不可少的。
