与肝外门静脉高压相关的先天性异常。
Congenital abnormalities associated with extrahepatic portal hypertension.
作者信息
Odièvre M, Pigé G, Alagille D
出版信息
Arch Dis Child. 1977 May;52(5):383-5. doi: 10.1136/adc.52.5.383.
Abstract
Congenital abnormalities were present in 12 out of 30 (40%) children with extrahepatic portal hypertension of unknown cause, but in only 2 out of 17 (12%) children with extnahepatic portal hypertension secondary to umbilical vein catheterization or omphalitis. The most frequent abnormalities in this series and in published reports were atrial septal defect, malformation of the biliary tract, and anomalous inferior vena cava. These findings are consistent with the view that some cases with extrahepatic portal hypertension are congenital in origin.
摘要
在30例病因不明的肝外门静脉高压患儿中，有12例（40%）存在先天性异常，但在17例继发于脐静脉插管或脐炎的肝外门静脉高压患儿中，仅有2例（12%）存在先天性异常。本系列研究及已发表报告中最常见的异常为房间隔缺损、胆道畸形和下腔静脉异常。这些发现与某些肝外门静脉高压病例起源于先天性的观点一致。
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