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[一名年轻无症状女性的病因不明的心肌脂褐质沉积症]

[Myocardial lipofuscinosis of unknown etiology in a young asymptomatic woman].

作者信息

Dolara A, Santoro G, Gori F

机构信息

Servizio di Cardiologia, Ospedale di Careggi, Firenze.

出版信息

Cardiologia. 1996 Mar;41(3):275-7.

PMID:8697485
Abstract

An asymptomatic 32-year-old woman was examined because of a family history of unexplained sudden deaths and a left ventricular strain pattern of the ECG during a routine examination. No abnormal finding of the cardiovascular system was present but an endomyocardial biopsy showed focal interstitial fibrosis, myocyte hypertrophy with heavy perinuclear accumulation of lipofuscin. The cause of these abnormalities remains unknown.

摘要

一名32岁无症状女性因有不明原因猝死家族史且在常规检查时心电图显示左心室劳损图形而接受检查。心血管系统未发现异常,但心内膜心肌活检显示局灶性间质纤维化、心肌细胞肥大且脂褐素在核周大量积聚。这些异常的原因仍不明。

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