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Leukocyte adhesion deficiency: report of a case and review of the literature.

作者信息

Lipnick R N, Iliopoulos A, Salata K, Hershey J, Melnick D, Tsokos G C

机构信息

Department of Pediatrics, Fairfax Hospital for Children, Falls Church, Virginia, USA.

出版信息

Clin Exp Rheumatol. 1996 Jan-Feb;14(1):95-8.

PMID:8697667
Abstract

Leukocyte adhesion deficiency (LAD) is a rare inherited immunodeficiency that is characterized by deficiency of the beta 2 integrin leukocyte adhesion molecules Mac-1, LFA-1, and p150,95. We describe a case of the severe form of LAD in an infant with recurrent infections and with a complete deficiency of beta 2 integrin molecules, and review the clinical aspects of the syndrome.

摘要

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Leukocyte adhesion deficiency: report of a case and review of the literature.
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2
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引用本文的文献

1
Defects in adhesion molecules.黏附分子缺陷。
Clin Rev Allergy Immunol. 2000 Oct;19(2):109-25. doi: 10.1385/CRIAI:19:2:109.