Suan C, Ojeda R, García-Perla J L, Pérez-Torres M C
Department of Paediatric Anaesthesia, Virgen del Rocío's Children's Hospital, Seville, Spain.
Paediatr Anaesth. 1996;6(3):231-3. doi: 10.1111/j.1460-9592.1996.tb00435.x.
Infants with Beckwith-Wiedemann syndrome usually present different abnormalities which may require surgical correction. Anaesthetic management may be complicated by abnormal airway anatomy, congenital heart disease and severe hypoglycaemia. Careful preoperative evaluation, perioperative monitoring and suitable choice of anaesthetic technique are required for a successful outcome. We report the perioperative management of a patient with Beckwith-Wiedemann syndrome presenting for omphalocoele surgery on his first day of life and for bilateral inguinal hernia repair four months later.
患有贝克威思-维德曼综合征的婴儿通常会出现不同的异常情况，可能需要进行手术矫正。气道解剖异常、先天性心脏病和严重低血糖可能会使麻醉管理变得复杂。为了取得成功的结果，需要进行仔细的术前评估、围手术期监测以及选择合适的麻醉技术。我们报告了一名患有贝克威思-维德曼综合征的患者的围手术期管理情况，该患者在出生第一天接受脐膨出手术，四个月后接受双侧腹股沟疝修补术。
