Cabrera A, Rodrigo D, Sáez F, Ramón Rumoroso J, Cabrera-Zubizarreta A, Pastor E
Servicio de Cardiología Pediátrica, Hospital de Cruces, Baracaldo.
Rev Esp Cardiol. 1996 May;49(5):346-52.
Patients with pulmonary atresia and a ventricular septal defect have one outlet vessel; the aorta. The pulmonary arteries may be present or absent, and there is a collateral shunt. Magnetic resonance imaging is used to study this.
We evaluated 10 patients with pulmonary atresia with ventricular septal defect. Five were males and the others were females, ages ranged between 1 day and 25 years, three patients were newborns. We used common planes, but mainly: axial-transverse and coronal, normal and right or left oblique projections.
The size of the ventricular septal defect was 1.75 +/- 0.67 cm (0.5-3.2). The pulmonary trunk was absent in 7 patients, it was atretic in 2 and it was present in one. Confluent pulmonary branches were seen in 6 patients (right 0.58 +/- 0.12, left 0.53 +/- 0.19), not confluent in 2 (with only one branch in each case) and absent in the other two. There was collateral shunt flowing from the descending aorta in 7 patients, from the ascending aorta in two and from the aortic in the final case. The ascending aorta was dilated in all cases (diameter 3.04 +/- 1.39), afterwards the relation between the ascending aorta and the descending aorta was 1.87 +/- 0.25. The aortic arch was right sided in 5 patients.
Magnetic resonance imaging is an alternative diagnostic method to angiocardiography. It gives complete information about the size, the position and the connection of the pulmonary arteries. It is also useful to evaluate the aortopulmonary to bronchial shunt.
患有肺动脉闭锁和室间隔缺损的患者有一条输出血管，即主动脉。肺动脉可能存在或缺失，并且存在侧支分流。磁共振成像用于对此进行研究。
我们评估了10例患有室间隔缺损的肺动脉闭锁患者。5例为男性，其余为女性，年龄在1天至25岁之间，3例为新生儿。我们使用了常规平面，但主要是：轴位 - 横断位和冠状位，正常以及右或左斜位投影。
室间隔缺损大小为1.75±0.67厘米（0.5 - 3.2厘米）。7例患者肺动脉干缺失，2例肺动脉干闭锁，1例肺动脉干存在。6例患者可见融合的肺分支（右侧0.58±0.12，左侧0.53±0.19），2例未融合（每种情况仅一个分支），另外2例缺失。7例患者有从降主动脉而来的侧支分流，2例来自升主动脉，最后1例来自主动脉弓。所有病例升主动脉均扩张（直径3.04±1.39），升主动脉与降主动脉的比例为1.87±0.25。5例患者主动脉弓位于右侧。
磁共振成像是心血管造影的一种替代诊断方法。它能提供有关肺动脉大小、位置和连接的完整信息。评估主肺动脉至支气管分流也很有用。
