囊性纤维化：CFTR 突变如何导致囊性纤维化？ - Suppr

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超能文献

Cystic fibrosis: How do CFTR mutations cause cystic fibrosis?

作者信息

Wine J J

机构信息

Cystic Fibrosis Research Laboratory, Stanford University, California 94305-2130, USA.

出版信息

Curr Biol. 1995 Dec 1;5(12):1357-9. doi: 10.1016/s0960-9822(95)00269-7.

DOI:10.1016/s0960-9822(95)00269-7

PMID:8749384

Abstract

摘要

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Cystic fibrosis: How do CFTR mutations cause cystic fibrosis?囊性纤维化：CFTR 突变如何导致囊性纤维化？

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[CFTR as cAMP-dependent chloride channels and as cAMP-dependent regulator of sodium channels].[囊性纤维化跨膜传导调节因子作为环磷酸腺苷依赖性氯离子通道及作为钠离子通道的环磷酸腺苷依赖性调节因子]

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