Levesque H
Service de Médecine Interne-Angiologie, CHU Rouen-Boisguillaume.
J Mal Vasc. 1996;21(2):80-3.
Several classifications have been proposed for erythermalgia according to causality (primary or secondary) or age of onset (presuming that all early-onset are primary). Recently a classification in three types of erythromelalgia have been proposed. Erythromelalgia and erythermalgia are defined as two independent and completely different disease entities. Clinically there are three different types of recurrent red, warm and burning pain in the extremities. That need to be distinguished for effective treatment according to their etiology: erythromelalgia in thrombocythaemia, primary erythermalgia and secondary erythermalgia. We recently observed 19 cases of erythermalgia; nine had primary erythermalgia; in 6 of 9, symptoms were relieved with aspirin. Ten of them had a secondary erythermalgia: 5 due to myeloproliferative disorders (erythromelalgia), 2 systemic lupus erythematosus and 3 to drugs. We used a two-level classification with a first level of primary or secondary erythermalgia, and a second level for primary erythermalgia, of familial or nonfamilial primary and for secondary erythermalgia, of thrombocythaemia disorders or other.
根据病因（原发性或继发性）或发病年龄（假定所有早发型均为原发性），已经提出了几种红斑性肢痛症的分类方法。最近有人提出将红斑性肢痛症分为三种类型。红斑性肢痛症和红斑热痛症被定义为两种独立且完全不同的疾病实体。临床上，四肢存在三种不同类型的反复出现的发红、发热和灼痛。为了根据病因进行有效治疗，需要对它们进行区分：血小板增多症中的红斑性肢痛症、原发性红斑热痛症和继发性红斑热痛症。我们最近观察了19例红斑热痛症患者；其中9例患有原发性红斑热痛症；在这9例中的6例中，症状通过阿司匹林得到缓解。另外10例患有继发性红斑热痛症：5例由于骨髓增殖性疾病（红斑性肢痛症），2例由于系统性红斑狼疮，33例由于药物。我们采用了两级分类法，第一级为原发性或继发性红斑热痛症，第二级对于原发性红斑热痛症，分为家族性或非家族性原发性，对于继发性红斑热痛症，分为血小板增多症相关疾病或其他。
