Reichert S, Berrod J P, Rozot P, Schmutz J L
Service de Dermatologie, Hôpital Fournier, Nancy.
J Fr Ophtalmol. 1996;19(5):389-94.
The naevus of Ota is a congenital pigmentary disorder usually involving the skin of the face in areas supplied by the first and second branches of the trigeminal nerve. Ipsilateral ocular melanosis is associated in 2/3 of the cases. The naevus occurrs most often in Asians. There have been 66 reported cases of malignant transformation of the naevus of Ota, generally affecting caucasians: 23 were melanomas of the eyeball (mostly of the choroid), and 13 were orbital melanomas. Only 4 cases of melanomas associated with a naevus of Ota without ocular melanosis have been previously described. We report a new case of orbital melanoma affecting a 30-year-old man. This melanoma complicated a right type III of Tanino naevus of Ota without ocular melanosis. The location of the tumor to the orbital apex and its extension to the spheno-cavernous area was responsible for an ipsilateral loss of vision without proptosis, which has not yet been described in any case of naevus of Ota without ocular melanosis.
太田痣是一种先天性色素沉着紊乱疾病，通常累及三叉神经第一和第二分支所支配区域的面部皮肤。三分之二的病例伴有同侧眼黑变病。太田痣最常发生于亚洲人。据报道，太田痣发生恶变的病例有66例，一般影响白种人：23例为眼球黑色素瘤（大多为脉络膜黑色素瘤），13例为眼眶黑色素瘤。此前仅描述过4例不伴有眼黑变病的太田痣相关黑色素瘤病例。我们报告1例眼眶黑色素瘤新病例，患者为一名30岁男性。该黑色素瘤并发于右侧III型谷野太田痣且无眼黑变病。肿瘤位于眶尖并延伸至蝶鞍海绵窦区，导致同侧视力丧失但无眼球突出，这种情况在既往任何不伴有眼黑变病的太田痣病例中均未被描述过。
