Repetto T, Procopio E, Materassi D, Favilli S, Jenuso R
Clinica Pediatrica I, Ospedale A. Meyer di Firenze, Italia.
Pediatr Med Chir. 1996 Mar-Apr;18(2):213-5.
Multiple hepatic hemangioendothelioma are vascular lesions of the liver that generally appear in the infancy with hepatomegaly, high output congestive heart failure and cutaneous hemangiomas. Many plans for management (steroid, radiation, hepatic artery ligation, embolization, cyclophosphamide) have been proposed. We report a case in two months old boy of hepatic hemangioendothelioma with arteriovenous shunts and heart congestive failure, successfully treated with steroid.
多发性肝血管内皮瘤是肝脏的血管病变,通常在婴儿期出现,伴有肝肿大、高输出量充血性心力衰竭和皮肤血管瘤。已经提出了许多治疗方案(类固醇、放疗、肝动脉结扎、栓塞、环磷酰胺)。我们报告一例两个月大患有肝血管内皮瘤并伴有动静脉分流和心脏充血性心力衰竭的男婴,经类固醇治疗成功。