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对于原发性纤毛运动障碍患者,切除支气管扩张灶是否有益?

Is resection of bronchiectasis beneficial in patients with primary ciliary dyskinesia?

作者信息

Smit H J, Schreurs A J, Van den Bosch J M, Westermann C J

机构信息

Departments of Pulmonary Diseases, St. Antonius Hospital, Nieuwegein, the Netherlands.

出版信息

Chest. 1996 Jun;109(6):1541-4. doi: 10.1378/chest.109.6.1541.

DOI:10.1378/chest.109.6.1541
PMID:8769508
Abstract

A retrospective study of 21 patients with primary ciliary dyskinesia (PCD) was done. Thirteen had prior resection of bronchiectasis and eight had not. Information about present complaints was obtained by a questionnaire. The prevalence of present respiratory symptoms was the same in both groups. The surgical patients had more severe disease and 85% of them considered the operation beneficial. Selected patients with PCD may have improved conditions with resection of bronchiectasis.

摘要

对21例原发性纤毛运动障碍(PCD)患者进行了一项回顾性研究。其中13例曾接受过支气管扩张切除术,8例未接受过。通过问卷调查获取了当前症状的信息。两组患者当前呼吸道症状的患病率相同。接受手术的患者病情更严重,其中85%的患者认为手术有益。部分PCD患者切除支气管扩张后病情可能有所改善。

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