Lee W T, Wang P J, Young C, Lai M W, Shen Y Z
Department of Pediatrics, College of Medicine, National Taiwan University, Taipei, R.O.C.
Pediatr Neurol. 1995 Nov;13(4):343-5. doi: 10.1016/0887-8994(95)00217-0.
A 10-year-old boy with Klippel-Feil syndrome had progressive atrophy of the left thenar eminence and absence of left radial pulse. Neurophysiologic studies and angiography were normal. However, duplex sonography over the wrists revealed an aberrant left radial artery. We speculate that the thenar atrophy in this patient is congenital, which may be due to the anomaly of the left radial artery, and is further compromised by vascular compression in the thoracic outlet.
一名患有克利珀尔-费尔综合征的10岁男孩出现左手鱼际肌渐进性萎缩且左侧桡动脉搏动消失。神经生理学研究和血管造影均正常。然而，手腕部的双功超声检查显示左侧桡动脉走行异常。我们推测该患者的鱼际肌萎缩是先天性的，可能是由于左侧桡动脉异常，并因胸廓出口处的血管受压而进一步加重。
