Rybojad M, Cambiaghi S, Moraillon I, Vignon-Pennmen M D, Morel P, Baudoin V, Loirat C
Service de Dermatologie, Hôpital Saint-Louis, Paris, France.
Br J Dermatol. 1996 Jul;135(1):124-7.
Omenn's reticulosis is an inherited severe combined immunodeficiency characterized by neonatal exfoliative erythroderma. A newborn baby who had minimal change nephrotic syndrome and Omenn's reticulosis is reported. Abnormalities in lymphocyte function could explain both the nephropathy and the cutaneous changes.