Cystic fibrosis: paediatric aspects.

With a comprehensive team approach and attention to early intervention, most infants with cystic fibrosis (CF) born in the 1990s will reach and contribute successfully to adult life. Our perception of CF has evolved from a lethal disease in childhood to a chronic disorder with increased mortality in adulthood. This article examines some of the issues involved in ensuring that children with CF achieve these goals, with special emphasis on the maintenance of health and the prevention of disease progression.