Abadoğlu O, Osma E, Uçan E S, Cavdar C, Akkoç N, Küpelïoğlu A, Akbaylar H
Chest Disease Department, Faculty of Medicine, Dokuz Eylül University, Izmir, Turkey.
Respir Med. 1996 Aug;90(7):429-31. doi: 10.1016/s0954-6111(96)90118-3.
Behçet's disease is a chronic multisystem vasculitis of unknown aetiology. This case report describes a patient who applied to the hospital because of dyspnoea, ascites, oedema of lower extremities and recurrent episodes of haemoptysis. For the last 12 yr, he had superior vena cava syndrome (SVCS) and cardiac and pulmonary involvement of Behçet's disease, and biochemical examination of ascite fluid yielded a chylous effusion containing triglyceride 421 mg dl-1 and cholesterol 49 mg dl-1. Chyloptysis was also detected by Sudan III stain. The patient died from cardiac tamponade in spite of cardiac fenestration. To the authors' knowledge, this is the first reported case of Behçet's disease with chylous ascites and chyloptysis in the English literature.
白塞病是一种病因不明的慢性多系统血管炎。本病例报告描述了一名因呼吸困难、腹水、下肢水肿和反复咯血而入院的患者。在过去12年里，他患有上腔静脉综合征（SVCS）以及白塞病累及心脏和肺部，腹水生化检查显示为乳糜性积液，甘油三酯含量为421mg/dl，胆固醇含量为49mg/dl。苏丹III染色也检测到乳糜咯血。尽管进行了心脏开窗术，患者仍死于心脏压塞。据作者所知，这是英文文献中首次报道的白塞病合并乳糜腹水和乳糜咯血的病例。
