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Spontaneous coronary artery rupture and cardiac tamponade in Ehlers-Danlos syndrome type IV.

作者信息

Evans R H, Fraser A G

机构信息

Department of Medicine, University of Wales College of Medicine, UK.

出版信息

Int J Cardiol. 1996 Jun;54(3):283-6. doi: 10.1016/0167-5273(96)02618-6.

DOI:10.1016/0167-5273(96)02618-6
PMID:8818754
Abstract

Spontaneous coronary artery rupture resulted in cardiac tamponade in a man with Ehlers-Danlos syndrome (type IV) presenting with acute onset of cardiac chest pain. Electrocardiograms suggested acute myocardial infarction. The haemopericardium was drained and angiography showed a ruptured distal branch of the left circumflex coronary artery. The patient remains well.

摘要

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A Lethal Complication after Coronary Angiography in a Patient with Ehlers-Danlos Syndrome.
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The role of postmortem study in the diagnosis of the cause of death in a young man: a rare case of Ehlers-Danlos syndrome type IV.尸检研究在一名年轻男性死因诊断中的作用:一例罕见的IV型埃勒斯-当洛综合征病例
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