Ozkan H, Ay N, Ozaksoy D, Ercal D, Erata Y, Durak H, Evyapan O, Toprak S
Department of Pediatrics, Dokuz Eylul University Faculty of Medicine, Izmir, Turkey.
Turk J Pediatr. 1996 Jan-Mar;38(1):113-7.
Congenital chylothorax is a rare condition in which chyle accumulates in the pleural space because of an intrauterine obstruction or anomalies of the thoracic duct. This paper presents a case of congenital chylothorax diagnosed antepartum echographically. The patient's history revealed a previous sibling with a similar diagnosis. The baby developed respiratory distress after delivery and the diagnosis was established by thoracentesis. Computed tomography of the chest and nuclear lymphangiography were obtained to evaluate the origin of the pleural effusion, but a congenital fistula or other pathology of the thoracic duct could not be demonstrated. Management of the baby consisted of ventilatory support in the delivery room, repeated thoracentesis and thoracostomy tube drainage, total parenteral nutrition and formula containing medium-chain triglycerides. The infant was discharged six weeks after birth in good condition.
先天性乳糜胸是一种罕见病症，由于宫内梗阻或胸导管异常，乳糜在胸腔内积聚。本文介绍了一例产前经超声诊断的先天性乳糜胸病例。患者病史显示其有一个曾被诊断为类似病症的兄弟姐妹。婴儿出生后出现呼吸窘迫，通过胸腔穿刺术确诊。进行了胸部计算机断层扫描和核素淋巴管造影以评估胸腔积液的来源，但未发现先天性瘘管或胸导管的其他病变。对婴儿的治疗包括在产房进行通气支持、反复胸腔穿刺和胸腔造瘘管引流、全胃肠外营养以及含中链甘油三酯的配方奶。婴儿出生六周后状况良好出院。
