Madhusudanan M, Gracykutty M, Cherian M
Department of Neurology, Medical college Hospital, Kottayam, India.
Acta Neurol Scand. 1995 Oct;92(4):308-12. doi: 10.1111/j.1600-0404.1995.tb00134.x.
Athetosis and dystonia are well known clinical signs, described in disorders of basal ganglia. As opposed to pseudoathetosis, true athetosis was hitherto not reported in cord lesions. We here report three patients with athetosis and dystonia of hands due to intramedullary lesions of cervical cord: two patients with syringomyelia and one with glioma. Even though pseudoathetosis can be produced by lesions of posterior columns and likely to be confused with the involuntary movements of our patients, they had clinical and EMG findings consistent with true athetosis. A possible explanation for the athetosis and dystonia due to cord lesion is being postulated.
手足徐动症和肌张力障碍是众所周知的临床体征，见于基底神经节疾病。与假性手足徐动症不同，真性手足徐动症迄今尚未见脊髓病变的报道。我们在此报告3例因颈髓髓内病变导致手部出现手足徐动症和肌张力障碍的患者：2例患有脊髓空洞症，1例患有神经胶质瘤。尽管后柱病变可引起假性手足徐动症，且可能与我们患者的不自主运动相混淆，但他们的临床和肌电图表现与真性手足徐动症一致。目前正在推测脊髓病变导致手足徐动症和肌张力障碍的可能原因。
