Simpson B B, Ryan D P, Donahoe P K, Schnitzer J J, Kim S H, Doody D P
Department of Pediatric Surgery, Massachusetts General Hospital, Boston 02114, USA.
J Pediatr Surg. 1996 Aug;31(8):1128-33. doi: 10.1016/s0022-3468(96)90101-3.
Complete laryngotracheoesophageal clefts (types III and IV) are rare congenital anomalies that occur when the primitive foregut fails to separate into the tracheobronchial tree and the esophagus. This article summarizes a 10-year institutional experience with six infants who had type IV clefts, presents a modification of the authors' surgical approach, and identifies pitfalls in the management of these infants. Three of the six children are long-term survivors. The recognition of specific complicating issues leads to a standardized approach, which can result in successful repair and long-term survival.
完全性喉气管食管裂(III型和IV型)是罕见的先天性畸形,发生于原始前肠未能分化为气管支气管树和食管之时。本文总结了本机构10年间对6例IV型裂患儿的治疗经验,介绍了作者手术方法的改进,并指出了这些患儿治疗中的陷阱。6名患儿中有3名长期存活。认识到特定的复杂问题可形成标准化治疗方法,从而实现成功修复和长期存活。