Pollak A, Friede R L
J Neuropathol Exp Neurol. 1977 Jul;36(4):712-25. doi: 10.1097/00005072-197707000-00006.
A survey of published cases of medulloepitheliomas indicates that this tumor is highly malignant (average course 6 months), occurs in early childhood (average age 4,4 years) and has no sex predilection. Although it may originate in any part of the central nervous system, it is most common in the cerebral hemispheres. The first case studied with the electron microscope is reported here. The fine structure of the tumor is similar to that of the fetal neural tube in showing a primitive epithelium having uniform nuclei rich in chromatin but little cytoplasm and sparse organelles; it rests on a distinct basement membrane. The epithelial surface lacks cilia or microvilli and is covered with an irregular amorphous coat which is probably the cause of the light-microscopic misinterpretation of an inner limiting membrane. The lateral cell surfaces lack interdigitations but show extensive primitive forms of cell junctions. The case presented is also unusual in being the second case on record originating in the cerebellum and the first showing massive seeding along the spinal canal.
对已发表的髓上皮瘤病例的一项调查表明,这种肿瘤具有高度恶性(平均病程6个月),发生于儿童早期(平均年龄4.4岁),且无性别偏好。虽然它可能起源于中枢神经系统的任何部位,但在大脑半球最为常见。本文报道了首例用电镜研究的病例。肿瘤的精细结构与胎儿神经管相似,表现为原始上皮,细胞核均匀,富含染色质,但细胞质少,细胞器稀疏;它位于一层明显的基底膜上。上皮表面没有纤毛或微绒毛,覆盖着一层不规则的无定形物质,这可能是在光镜下误将其解释为内界膜的原因。细胞侧面缺乏指状交叉,但显示出广泛的原始细胞连接形式。所报道的该病例也很不寻常,它是有记录以来第二例起源于小脑的病例,也是第一例显示沿椎管大量播散的病例。